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eRAM

encyclopedia of Rare Disease Annotation for Precision Medicine




Disease granulomatosis with polyangiitis
Symptom C0042384|vasculitis
Sentences 8
PubMedID- 21147630 According to the american college of rheumatology (acr), classification criteria of the css are: small vessel vasculitis along with wegener's granulomatosis (wg), microscopic polyangiitis (mpa), and idiopathic necrotizing crescentic glomerulonephritis ncgn 3.
PubMedID- 22247758 Evidence is lacking for direct pathogenicity of human anti-proteinase-3 (pr3) antibodies in development of systemic vasculitis and granulomatosis with polyangiitis (gpa, wegener's granulomatosis).
PubMedID- 21876314 He was diagnosed with antineutrophil cytoplasmic antibody-associated vasculitis due to wegener granulomatosis, microscopic polyangiitis, or drug induction.
PubMedID- 20695860 Granulomatous vasculitis is classically associated with wegener's granulomatosis, lymphomatoid granulomatosis or churg-strauss syndrome.
PubMedID- 25859349 Anti-neutrophil cytoplasmic antibody (anca)-associated vasculitis includes granulomatosis with polyangiitis (wegener's granulomatosis) and microscopic polyangiitis.
PubMedID- 25390916 Purpose: the purpose of this study was to report the use of plasmapheresis in the management of choroidal vasculitis associated with wegener granulomatosis.
PubMedID- 23480833 Expert opinion: small-vessel anti-neutrophil cytoplasmic antibody (anca)-associated vasculitis, especially granulomatosis with polyangiitis (wegener's granulomatosis) are the most frequent causes of pulmonary vasculitis and typically present as nodules, alveolar infiltrates (haemorrhagic or not), cavities or tracheobronchial stenosis.
PubMedID- 25332635 vasculitis like granulomatosis with polyangitis (wegener's granulomatosis), churg strauss syndrome and sarcoidosis, which are the second consideration, are ruled out by serological investigations.

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